Multimodality Imaging in an Adult Patient with Scimitar Syndrome
نویسندگان
چکیده
The "Scimitar syndrome" is a rare congenital anomaly characterized by combination of partial or complete pulmonary venous return from the right lung to the inferior vena cava either above or below the diaphragm together with hypoplasia of the right lung and sometimes systemic arterial supply to the right lung. In this case, multimodality imaging findings such as the vein draining into the inferior vena cava, the presence of hypertrophied and dilated right ventricle, the absence of other cardiac abnormalities, displacement of the heart without malrotation and the mediastinum to the right, normal bronchial and vascular continuity in the whole lung, absence of pulmonary sequestration and systemic collaterals, normal perfusion and systolic functions of the left ventricle were reported.
منابع مشابه
Scimitar Syndrome in an Asymptomatic Adult: Fortuitous Diagnosis by Imaging Technique
Congenital cardiopathies in adults are a rare clinical entity in the cardiology consultations. Advances in imaging techniques allow the fortuitous diagnosis of mild forms of these congenital abnormalities. We describe a case of an asymptomatic 41-year-old man, with a medical history of recurrent pneumonia during childhood and an established diagnosis of scimitar syndrome by computed tomography.
متن کاملScimitar Syndrome: Pathology, Clinical Presentation, Radiographic Features, and Treatment
Scimitar syndrome is characterized by partial or total anomalous pulmonary venous return from the right lung along with pulmonary hypoplasia.Wesearched the mail databases such as Medline (via PubMed), Scopus and EMBASE and Google Scholar. Diagnosing infantile scimitar syndrome requires meticulous attention and high suspicion of the early referral and management. The association of the syndrome ...
متن کاملMultimodality imaging of anomalous pulmonary veins
Partial anomalous pulmonary venous connection (PAPVC) is an extremely rare congenital condition where one or more of the pulmonary veins are connected to the venous circulation. Although initially suspected with unexplained right ventricular enlargement on transthoracic echocardiography (TTE), cardiac MRI is able to delineate the anatomical variant. We present a case of a 65-year-old male diagn...
متن کاملUncommon Cause of Paradoxical Embolism in a Case of Scimitar Syndrome
Scimitar syndrome, a rare congenital cardiopulmonary condition, presents in both pediatric and adult populations as an anomalous pulmonary venous return of most of the right lung to the inferior vena cava. Recently, asymptomatic adult cases have been diagnosed with advances in imaging studies. We report the case of an asymptomatic 43-year-old male, with a complex variant scimitar syndrome diagn...
متن کاملMediastinal lung herniation in an adult patient with Scimitar syndrome.
Early cardiac abnormalities in obese children: importance of obesity per se versus associated cardiovascular risk factors. Delle Donne MG et al. Obesity cardiomyopathy: is it a reality? An ultrasonic tissue characterization study. Abnormal myocardial deformation properties in obese, non-hypertensive children : an ambulatory blood pressure monitoring, standard echocardiographic, and strain rate ...
متن کامل